Our patient is a 20 year old boy with severe maxillary hypoplasia with a history of bilateral cleft lip and palate. We performed a maxillary advancement with distraction osteogenesis.
Nikhil Kamath, BS
Aaron Smith, MD
Michael S. Golinko, MD
Kumar Patel, PA-C
Le Fort I Osteotomy with Distractor
The patient was laid supine after successful nasal endotracheal intubation. Maxillary exposure was gained through mucosal incision from 1st premolar to 1st premolar. A 5mm gingivobuccal cuff is maintained. The maxilla is degloved with a number 9 periosteal elevator. Care is taken to identify infraorbital nerve on each side.The mucosa is lifted from the periform appature using a Penfield 1. The posterior foot plate is fitted bilaterally prior to osteotomy. This distractor body is parallel and confirmed to both be in an appropriate vector. The maxilla is marked for osteotomy. Reciprocating saw is used lateral to medial taking extra caution over the thin walled maxillary sinus. Olive osteotome is used to separate mucosa from the posterior palate. Kowamoto osteotome is used at pterygomaxiallary junction. Ribbon Osteotome is used to complete posterior wall osteotomies and complete the maxilla down fracture. Once the maxilla is confirmed to be completely free, fixation of anterior and posterior foot plates is finalized. The distractor bodies are turned to begin distraction osteogenesis. The gingovobuccal incision is closed with running 3-0 chromic suture. The patient was extubated in good condition
Severe maxillary hypoplasia (>10mm of advancement required)
No absolute contraindications, but conventional fixed advancement remains the standard of care in patients of skeletal maturity with mild to moderate maxillary hypoplasia.
-Orthodontic preparation
-Low dose craniofacial CT scan with 3D reconstruction
-Virtual surgical planning
-Sterolithic skull model used to modify distractor footplates
Benefits over conventional Le Fort I advancement:
-helpful in cleft lip/palate population with poor bone quality and scaring from previous surgery
-lower risk of disharmony than combined maxillary advancement with mandibular setback
-skeletal maturity not required for distraction osteogenesis
-relative long-term stability in pts who have failed traditional advancement
-decreased relapse rate compared to the conventional advancement
-Infection/bleeding
-Horizontal relapse (risk highest within 6 months of consolidation)
-Decreased ANB angle in patients who have not reached skeletal maturity
-Negative effect on velopharyngeal competence
None
Arkansas Children's Hospital Department of Pediatric Craniofacial Plastic Surgery
Mild eyelid ptosis with good elevator function can be treated with minimally invasive procedures. When Muller’s muscle contraction corrects the deficiency (evaluated by phenilefrine test) conjunctivo-mullerectomy is the procedure of choice.
This video presents the surgical steps to perform conjunctivo-mullerectomy.
Contributors
Dov Charles Goldenberg, MD Phd, Division of Plastic Surgery, Hospital das Clinicas, University of Sao Paulo Medical School
Vania Kharmandayan, MD, Division of Plastic Surgery, Hospital das Clinicas, University of Sao Paulo Medical School
This video outlines the steps taken for pre-operative markings that need to be made prior to performing unilateral cleft lip repair using the Fisher anatomic subunit approximation technique. The technique has been written about in detail by Dr. David Fisher in his article “Unilateral Cleft Lip Repair: An Anatomical Subunit Approximation Technique”. This video simply outlines the markings that are made prior to performing this technique, which are crucial for correctly carrying out the repair.
Review Le Fort I Osteotomy with placement of Distractor.